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DeCS
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Descriptor English:
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Immunoglobulin G4-Related Disease
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Descriptor Spanish:
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Enfermedad Relacionada con Inmunoglobulina G4
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Descriptor Portuguese:
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Doença Relacionada a Imunoglobulina G4
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Synonyms English:
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Autoimmune Disease, IgG4-Associated
Autoimmune Diseases, IgG4-Associated
G4-Related Disease, Immunoglobulin
G4-Related Diseases, Immunoglobulin
IgG4 Associated Autoimmune Disease
IgG4 Related Disease
IgG4 Related Systemic Disease
IgG4-Associated Autoimmune Disease
IgG4-Associated Autoimmune Diseases
IgG4-RD
IgG4-Related Disease
IgG4-Related Diseases
Immunoglobulin G4 Related Disease
Immunoglobulin G4-Related Diseases
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Tree Number:
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C20.111.572
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Definition English:
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A spectrum of systemic autoimmune diseases in which IMMUNOGLOBULIN G4 plays a pathophysiologic role. It can affect multiple organs in highly variable presentations, characterized by inflammatory lesions composed of IgG4-positive PLASMA CELLS, further infiltrated by T helper cells (T-LYMPHOCYTES, HELPER-INDUCER) when linked to progressive FIBROSIS and eventual organ damage. |
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History Note English:
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2019
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Allowable Qualifiers English:
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Record Number:
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57738
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Unique Identifier:
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D000077733
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Occurrence in VHL:
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Similar:
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DeCS
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